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Surgical Management of Omphalocele: A Plastic Surgeon’s Perspective Brian I. Labow, MD, FACS, FAAP...
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Transcript of Surgical Management of Omphalocele: A Plastic Surgeon’s Perspective Brian I. Labow, MD, FACS, FAAP...
![Page 1: Surgical Management of Omphalocele: A Plastic Surgeon’s Perspective Brian I. Labow, MD, FACS, FAAP Department of Plastic Surgery Children’s Hospital Boston.](https://reader035.fdocuments.us/reader035/viewer/2022081506/56649e215503460f94b0d65b/html5/thumbnails/1.jpg)
Surgical Management of Omphalocele: A Plastic Surgeon’s Perspective
Brian I. Labow, MD, FACS, FAAP
Department of Plastic SurgeryChildren’s Hospital Boston
Harvard Medical School
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![Page 3: Surgical Management of Omphalocele: A Plastic Surgeon’s Perspective Brian I. Labow, MD, FACS, FAAP Department of Plastic Surgery Children’s Hospital Boston.](https://reader035.fdocuments.us/reader035/viewer/2022081506/56649e215503460f94b0d65b/html5/thumbnails/3.jpg)
• Heterogenous population and associated anomalies common
• Many approaches, techniques and tools
• No single approach will suit all patients
• Outcome data based limited by numbers and confounding variables
IntroductionIntroduction
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• General considerations• Tools/techniques • Adjuvant procedures• Summary
OutlineOutline
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• Usually not an emergency• Most cases can be
managed with “conventional approaches”
• Circumstances may mandate change in course…
General Comments
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• Medically unstable• Damage control (e.g. ruptured
membrane, silo disruptions)• Incomplete reduction • Extreme visceral-peritoneal
disproportion
Clinical Situation?
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Tools and TechniquesTools and Techniques
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• NPWT/VAC™ hopefully not necessary!
• Decrease edema and bacterial colonization accelerate granulation
• Used with absorbable mesh, biological fascial substitute
• Bridge to definitive reconstruction (Kilbride et al. J Ped Surg (2006) 41, 212–215)
Negative-Pressure Wound Therapy Negative-Pressure Wound Therapy
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• Mechanical process to increase surface area of adjacent tissues
• Examples: Growth, Silo, External Skin closure devices
• Adjunct to flap transfer• Progressive process takes time
Tissue-ExpansionTissue-Expansion
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• Tissue expanders require a clean field with minimal inflammation
• Epidermis thickens, dermis and fat atrophy, muscle thins, angiogenesis
• Multiple expanders, small, frequent fillings
Tissue-ExpandersTissue-Expanders
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• Subcutaneous, submuscular and intraperitoneal placement all reported
• Small case series, longest follow-up 3 yrs
Tissue-ExpandersTissue-Expanders
(Tanenbaum et al. Plas Rec Surg (2007)120,1564–7)
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• Useful in a subset of patients• Additional GA, time and good local
tissue conditions required• Judgment in rate of expansion• Extrusion and infection most
frequent complications
Tissue-ExpandersTissue-Expanders
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• Relaxing incision(s) separating rectus sheath from ext obliq aponeurosis
• Autologous tissue, 1-stage• Skin deficit?• Large experience in adults
Component SeparationComponent Separation
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• 1 series of 10 consecutive omphalocele patients (mean age 6.5 months) Van Eijck et al. J Ped Surg (2008)
• Mean defect size 8 cm• Required temporary prosthetic in 1 case• Complications in 3 patients (skin necrosis,
hematoma, infection)• Mean follow-up 2 years, no hernias
Component SeparationComponent Separation
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• Usually a lifeboat• Allows egress of fluid,
visualization of bowel• Used with NPWT • Lasts 3-4
months….hernia• Cost Vicryl™ 15x 15”
$1800*
Absorbable MeshAbsorbable Mesh
* BCH list price 2013
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• Allows tissue ingrowth, stronger
• Higher rate of enterocutaneous fistulae
• Onlay support• Cost e.g. Marlex™
10x14” $500
Non-absorbable, MeshedNon-absorbable, Meshed
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• Temporary use silo construction (e.g. Silastic™)
• No ingrowth, minimal adhesions
• Permanent use (e.g. Goretex™) higher hernia rate?
• Cost* $600 for 10x15”Goretex™
Non-absorbable, Non-meshedNon-absorbable, Non-meshed
* BCH list price 2013
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• Variety of freeze-dried, acellular dermal or intestinal products (e.g. Alloderm™, Surgisis™)
• Inlay graft or onlay above fascia
• Neovascularized, tissues replaced by native cellular ingrowth
Biological MaterialsBiological Materials
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• Small series/case reports in pediatric literature (Alaish et al. J Ped Surg (2006) 41, E37–E39)
• Variable reports in adult abdominal wall reconstruction literature
• Cost has come down, 5x10” sheet of Alloderm™ ~$1800*
Biological MaterialsBiological Materials
* BCH list price 2013
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• Local tissues usually sufficient
• Mobilization wide undermining
• Can be facilitated with relaxing incisions
FlapsFlaps
Zama et al. Br Assoc Plas Surg (2004) 57, 749–753
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FlapsFlaps
Br Assoc Plas Surg (2004) 57, 749–753
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• Skin closure: secondary but important part of reconstruction
• Umbilicoplasty if possible
• Secondary procedures: hernias, bulges, hypertophic/depressed scar
Adjunctive ProceduresAdjunctive Procedures
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Adjunctive ProceduresAdjunctive Procedures