R. Mark Ray, M.D. Director: Children’s Hospital Cleft and Craniofacial Team East Tennessee...

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R. Mark Ray, M.D. Director: Children’s Hospital Cleft and Craniofacial Team East Tennessee Children’s Hospital

Transcript of R. Mark Ray, M.D. Director: Children’s Hospital Cleft and Craniofacial Team East Tennessee...

Page 1: R. Mark Ray, M.D. Director: Children’s Hospital Cleft and Craniofacial Team East Tennessee Children’s Hospital.

R. Mark Ray, M.D.

Director: Children’s Hospital Cleft and Craniofacial Team

East Tennessee Children’s Hospital

Page 2: R. Mark Ray, M.D. Director: Children’s Hospital Cleft and Craniofacial Team East Tennessee Children’s Hospital.

Evaluation and Treatment of the Child With Cleft Lip and

Palate – Team Care

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Disclosure Statement of Disclosure Statement of Financial InterestFinancial Interest

I, R. Mark Ray M.D.I, R. Mark Ray M.D.,,

DO NOT DO NOT have a financial have a financial interest/arrangement or affiliation with interest/arrangement or affiliation with one or more organizations that could one or more organizations that could be perceived as a real or apparent be perceived as a real or apparent

conflict of interest in the context of the conflict of interest in the context of the subject of this presentation. subject of this presentation.

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Pediatric Facial Anomalies Team Surgeon Speech Therapist Audiologist Nursing Pediatrician Orthodontist Social Work Nutritionist

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Classification- Cleft Lip

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Median clefts

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Mandibular Cleft

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Unilateral Lip RevisionInsufficient Advancement

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Prenatal Diagonosis Provide information

to families and answer questions

Prepare family for feeding their baby

Link family to resources

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Orthodontic Treatment

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Alveolar Ridge Bone Grafting

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Bardach, Janusz Salyer & Bardach’s Atlas of Craniofacial & Cleft Surgery. Volume II. Lippincott – Raven ; Philadelphia 1999

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Palate Expansion

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Subtle Alveolar Defect

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Alveolar Ridge Bone Grafting

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Alveolar Ridge Bone Grafting

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Alveolar Ridge Bone Grafting

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Speech Issues Velopharyngeal

Insufficiency

Compensatory errors

Articulation Disorder

Velocardiofacial Syndrome

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Rhinoplasty

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Cleft and Craniofacial Surgeries: 2009 & 2010

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Pierre Robin Sequence and Distraction Osteogenesis in the Neonatal Period

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Nager Syndrome

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Overview Retrognathia, Glossoptosis, Cleft Palate 1 in 9000 live births Mortality 5-30% Airway and feeding difficulties are

presenting problems Management is not uniform

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Tongue base obstruction

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Positioning

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Positioning

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Tracheostomy: Disadvantages

Complications: Cannula obstruction Accidental

decannulation Mortality significant Average age

atdecannulation: 3.1 years!

Functional Impairment

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Distraction Osteogenesis

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Distraction Osteogenesis

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Distraction OsteogenesisInternal Device

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Distraction Osteogenesis

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Airway Before and After

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Occlusion

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Distraction Osteogenesis

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Judy Marciel Cleft Team Coordinator Feeding and Nutrition Specialist Provider and Family Education Outcomes Evaluation and Analysis Research Coordinator Contact :

865-541-8510

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Questions