OSTEOCHONDROMA
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Transcript of OSTEOCHONDROMA
OSTEOCHONDROMA
• Cartilage capped exostosis
• Commonest benign tumour of bone
• Metaphyseal developmental abnormality
D FRANTZEN OSTEOCHONDROMA
INCIDENCE• 45 % of benign bony tumours
• 12 % of all bony tumours
• Become evident < 20 yrs
• Solitary or multiple
• Any enchondral ossification bone
D FRANTZEN OSTEOCHONDROMA
CLINICALLY
• Lump or mechanical problem
• Tendon or nerve irritation
• Sessile or pedunculated
• 50% distal femur, proximal tibia, proximal humerus
D FRANTZEN OSTEOCHONDROMA
CLINICAL
• Active growth during puberty
• Move towards diaphysis during growth
• Excise if troublesome in second decade
D FRANTZEN OSTEOCHONDROMA
RADIOLOGY
• Flat/ sessile / pedunculated
• Tumour blending into metaphysis
• Pedunculated orientated proximally
• Cartilage cap with calcification
D FRANTZEN OSTEOCHONDROMA
PATHOLOGY
• Normal bone covered by normal cartilage cap
• Cartilage cap resembles normal growth plate
• Cartilage more disorganized
D FRANTZEN OSTEOCHONDROMA
PATHOLOGY
• Covered by thin layer of periosteum
• Binucleate chondrocytes in lacunae
D FRANTZEN OSTEOCHONDROMA
TREATMENT
• Nil required unless symptomatic
• Extra-capsular marginal excision
• Recurrence < 5%
D FRANTZEN OSTEOCHONDROMA
PROGNOSIS
• Risk of malignancy if solitary - 0.2 %
• Risk of malignancy in diaphyseal aclasia : - 20 %
• Sarcomatous changes usually low- grade
D FRANTZEN OSTEOCHONDROMA