KARLA SANTOS-JASSO, M.D. · 1.Redo PSARP with previous colostomy 2.PSARP 3.Malone procedure after...

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KARLA SANTOS-JASSO, M.D. National Institute of Pediatrics Mexico City, Mexico May 2018.

Transcript of KARLA SANTOS-JASSO, M.D. · 1.Redo PSARP with previous colostomy 2.PSARP 3.Malone procedure after...

Page 1: KARLA SANTOS-JASSO, M.D. · 1.Redo PSARP with previous colostomy 2.PSARP 3.Malone procedure after successful bowel management with enemas 4.I don’t know. We performed a Malone procedure

KARLA SANTOS-JASSO, M.D.National Institute of Pediatrics

Mexico City, MexicoMay 2018.

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9-year-old female patient

• Referred to us due to fecal incontinence

Past Medical History

• Anorectal malformation with recto vestibular fistula• Primary PSARP (5 days after birth)

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q Anus within the center of the sphincter

q Dilation was made with Hegar number 13 (at the anus level, it allowed a 15 Hegar, but it was not possible to progress beyond 1.5 cm)

Clinical appearance

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X-ray

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The patient can´t pass stool and gas through rectum

We performed three enemas (500 ml saline solution)

One enema per day

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SIAP0.96

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Contrast enema

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What is your diagnosis?

1. Constipation associated with anorectal malformation

2. We need to rule out Hirschsprung disease with rectal biopsy

3. Acquired stenosis of the rectum4. Fecal incontinence secondary to anorectal

malformation5. I don´t know

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Acquired stenosis of the rectum

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We started laxative: senna tablets 8.6 mgWe increased doses until 6 tablets (51.6 mg)

every day in a single dose

17.2 mg(2 tab)

No fecal evacuation + abdominal

pain

Enema followed by 34.4 mg (4

tab) + paracetamol

No fecal evacuation + abdominal

pain

Enema followed by 43 mg (5 tab) + paracetamol

No fecal evacuation + abdominal pain

Enema followed by 51.6 mg (6 tab) +

paracetamol

No response (fecal impaction “colonic impaction” +

abdominal pain all day)

We indicated one enema daily (500 ml saline solution)

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We indicated one enema daily (500 ml saline solution)

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Weperformedrectaldilationsunderanesthesia.Maximumdilateddiameter16Hegar (operatingroom)

Butintheclinicandathome,sheneverdilatedmorethanHegar 13,becauseofpain.

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Looking at this stenosis of the rectum, which procedure do you

think this patient needs?

1. Redo PSARP with previous colostomy 2. PSARP 3. Malone procedure after successful bowel

management with enemas 4. I don’t know

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We performed a Malone procedure by laparoscopy…

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Currently, patient is on daily enema (500 ml saline solution).

No accidents, and when she has had episodes of diarrhea she is

fecally continent. Clinical follow-up time is 22 months

Thank youKarla Santos-Jasso MD

[email protected]