Ingrid Natali

Vannessa Mendez

Margarita Chen

1st Period

Anatomy Honors

Short, incompletely developed tongue Can occur either as an isolated malformation or an association with other

deformities common in Hanhart’s Syndrome such as• Hypodactylia • Peromelia• Micrognathia

Underdeveloped tongue Feeding problems Breathing problems Speech problems Swallowing problems Missing teeth Tooth enamel defects

12th cranial nerve is affected (hypoglossus) Spleen and gonads Arms Hands Jaws and face

The patient was a 6-year-old boy diagnosed with hypoglossia-hypodactylia syndrome at birth.

Speech therapy Orthodontic treatment. Compliance with an

orthodontics treatment plan is essential to prevent complications such as collapse of the bite especially if there are missing teeth.

Breathing assistance may be needed early in life

Generally patients can expect a good prognosis. Early management of problems with breathing, swallowing, feeding, speech as well as orthodontic management can enable a patient to lead a relatively normal life.

Robert-Gnansia, E. (2005, July). orpha.net. Retrieved February 7, 2012, from http://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=EN&Expert=989

Hypoglossia. (2011). RightDiagnosis. Retrieved February 7, 2012, from http://www.rightdiagnosis.com/h/hypoglossia/intro.htm

Hanhart Syndrome. (n.d.) University of Kansas Hospital. Retrieved February 7, 2012, from http://www.kumed.com/healthwise/healthwise.aspx?DOCHWID=nord1022

"An Error Occurred Setting Your User Cookie." An Error Occurred Setting Your User Cookie. N.p., n.d. Web. 7 Feb. 2012. <http://www.cpcjournal.org/doi/pdf/10.1597/1545-1569(2003)040%3C0196:ROAPWH%3E2.0.CO;2>.

"The hypoglossia—hypodactylia syndrome: Report of 2 cases 10.1016/0030-4220(81)90150-X : Oral Surgery, Oral Medicine, Oral Pathology | ScienceDirect.com." ScienceDirect.com | Search through over 10 million science, health, medical journal full text articles and books.. N.p., n.d. Web. 7 Feb. 2012. <http://www.sciencedirect.com/science/article