Eritema discromico pertans
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Transcript of Eritema discromico pertans
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Hipermelanosis ideopatica
› Adquirida, generalizada
› Macular, azul grisaceo ceniciento
Otro nombres:
› Dermatitis cenicienta o Cinderella Dermatits
› Ashy dermathosys
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+ America Latina y Asia
Descrita en El Salvador
› Oswaldo Ramirez 1957
Individuos de piel oscura tipo IV
Mujeres: cualquier edad, 2º decada
Factores geneticos:
› Poblaciones
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Etiologia: desconocida
Factores predisponentes:
› Ingestion de Nitritos de amonio
› Parasitosis intestinales: nematodos
› Medios de contraste
› Alergia al cobalto
› Exposicion al clorotanolil
› Carcinoma bronquial
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Estadio temprano: reaccion inflamatoria
› Agente ambiental
Hiperpigmentacion persistente
Anormalidad inmunologica
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Queratino-citos
• Expre-sionAg
Cel. Dendriticas
• Ag OKT4 y OKT 6
Infiltrado dermico
• CKT 4 y CKY 8 +
• Cuerpos colioides
• DepositosIgG
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Asisntomatica
Importancia Cosmetica
Larga evolucion: 3m-12ª
Afecta tronco, brazo, cuello, cara
Respeta: palma, planta, uñas mucosas
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Simetrica
Manchas azul grisaceas
0.5cm a varios cm
Activa: bordes eritematosos
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Carvajal y colaboradores:
1. Dermatitis Cenicienta Castaña
› Localizacion espeficida
› Manchas ceniza
› Inicialmente Cara, V escote
› Parte alta de dorso
› MS, muslos, piernas
› Manchas numulares
› Cambian: castaño
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2. Dermatitis Cenicienta numular
› Formas circulares, elipsoidales
› Independientes
› Escasas o abundantes
› 5 mm a 2cm
› Pecho, espalda
› Abdomen, MS
› Color gris
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No existe ninguno
› Laboratorio
› gabinete
Histologia
› Reaccion liquenoide atipica
› Edema focal Cel. Basales
› Incontinencia pigmenti
› Infiltrado inflamatorio
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Diferenciar:
› Melodermias friccionales
› Liquen plano pigmentado
› Eritema pigmentado fijo
› Lepra tuberculoide
› Liquen pigmentogenico
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Muchas opciones:
› Pocas dan resultados
Corticoides topicos
Fosfato de cloroquina
Griseofulvina
Protectores solares
Hidroquinona 5-15%
Exfoliacion quimica
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