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Aneurismas de la vena de galeno
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Transcript of Aneurismas de la vena de galeno
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aneurisma de la vena de galenoaneurisma de la vena de galeno
jaime diegopérez ramírezjefe neurocirugia
hospital de pediatría del centro medico nacional siglo xxi
Instituto Mexicano del Seguro Social
jaime diegopérez ramírezjefe neurocirugia
hospital de pediatría del centro medico nacional siglo xxi
Instituto Mexicano del Seguro Social
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• sinonimia:
• aneurisma varicoso
• aneurisma de la ampolla
• malformación
• fístula arteriovenosa
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• Even when the disease has been recognized as a congenital condition, was first described in an adult of 49 years by Steinhel in 1895
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• Clinically 3 different types:
• Newborn presentation ( high mortality)
• Infants (prominent veins and hydrocephalus)
• Adolescence and adults
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Clinical data
• Newborn
• Macrocephaly
• Prominent frontal vein
• Holosystolic trill
• Cardiac failure
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Clinical data
• Infant
• Hydrocephaly
• Mild intelectual deficit
• Epilepsy
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• Epilepsy
• Mild neurocognitive deficit
• headache?
• Espontaneous hemorrage?
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Clasification
• Thalamic AVM adyacent to
• AV Fistulae ChoroidalChoroidal
MuralMural
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choroidal
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mural
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Clinical progression
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Prognostic Scale
Less than 8: poor prognosis, no treatment9 to 12 more than 50% of survivors if treated acutely
Above 12 good prognosis, programed intervention
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Diagnostic studies
• Ultasound prenatal and neonatal
• IRM with angiography
• Angiography (interventional)
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treatment
• Until 20th century by 40’s it was no treatment but in 1945 it was the first AVC (abrir, ver y cerrar) surgery
• In 60’s was first described the 3 different prognostic groups.
• Surgery era between 70’ and 80’ the surgical era
• Latest 80’ and early 90’s endovascular embolization
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Surgery
• There’s no efective surgical treatment
• clipping feeders
• Shunting (not recomended)
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Embolization
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Embolization
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centro medico nacionalsiglo xxi
• 6 casos
• 4 neonatal presentation
• 3 die, 1 lost in following