Cardiac CT in Adult Congenital Heart Disease ·  · 2013-12-05Cardiac CT in Adult Congenital Heart...

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Transcript of Cardiac CT in Adult Congenital Heart Disease ·  · 2013-12-05Cardiac CT in Adult Congenital Heart...

Cardiac CT in Adult Congenital Heart Disease

DENNIS FOLEY

MEDICAL COLLEGE WISCONSIN

Adult CHD

AORTIC ANOMALIES COARCTATON , PDA

TRANSPOSITION MUSTARD

BAFFLE LEAK, STENOSIS RT VENTRICLE FAILURE

JANTENE ARTERIAL SWITCH CORONARY , PULMONARY STENOSES

TETRALOGY FALLOT POST CORRECTION PV INSUFFICIENCY

FONTAN STENOSES, PULMONARY EMBOLI CONGESTIVE HEPATOPATHY, CARDIAC CIRRHOSIS

Aortic Coarctation

ISSUES DELAYED

DIAGNOSIS

POST TREATMENT SURVEILLANCE

POST TREATMENT COMPLICATIONS

PSEUDO COARCTATION ASCENDING AORTIC GRAFT

POST AORTOPLASTY

COARCTATION ENDOSTENT

LEFT SUBCLAVIAN FLAP AORTOPLASTY

Transposition SURGICAL CORRECTION

AND COMPLICATIONS

MUSTARD/SENNING ATRIAL BAFFLE BAFFLE LEAK/

STENOSIS

RVF

JANTENE ARTERIAL SWITCH CORONARY,

PULMONARY STENOSES

RV

LV

SYSTEMIC ATRIUM

PULMONARY ATRIUM

TV

RV

SYSTEMIC ATRIUM

TGV , MUSTARD, PACEMAKER LEADAO

RVOT

LV

TV

SA

TRANSPOSITION MUSTARD PROCEDURE

LAD

RCA

UPPER EXT VEIN INJECTION

BAFFLE STENOSIS , LEAK

AZYGOS VEIN

IVC

SECOND INJECTION DELAYED ACQUISITION

RV

AO

PA

LVLV

JANTENE ARTERIAL SWITCH

PA

AS AORV

RA

LA

FRONTAL

MPA

RPA

LPA

TRANSPOSITION ARTERIAL SWITCH

MPA

MPA

LCARCA

JANTENE ARTERIAL SWITCH

Tetralogy of Fallot

INITIAL PALLIATIVE REPAIR BLALOCK TAUSSIG

WATERSTON, POTTS SHUNTS

DEFINITIVE REPAIR INFUNDIBULECTOMY

VSD CLOSURE

COMPLICATIONS PULMONARY

REGURGITATION

PA

TETRALOGY FALLOT, INFUNDIBULECTOMY VSD REPAIR , PULMONARY VALVE INSUFFICIENCY

CONUS BRANCH RCA

Fontan Procedure

ATRIO PULMONARY CONNECTION

CAVO PULMONARY INTRACARDIAC ( LATERAL TUNNEL )

EXTRACARDIAC

FONTAN PROCEDURE EXTRA CARDIAC CAVO PULMONARY

SIMULTANEOUS UE/IVC INJECTION

NUTMEG LIVER

CARDIAC CIRRHOSIS

CARDIAC CIRRHOSIS

REGENERATIVE NODULE

Summary

300,000 ACHD PATIENTS IN UNITED STATES

MEDICAL CARE AND SUPERVISION SPREAD BETWEEN SPECIALISED CENTERS AND PHYSICIAN PRACTICES

ROLE OF CT IMAGING THORACIC AORTA CORONARY ANOMALIES AND STENOSES STRUCTURAL ISSUES WITH PRIOR REPAIRS EXTRA CARDIAC ISSUES eg FONTAN

HEPATOPATYHY